Résumé

Fibrosing mediastinitis (FM) is a rare, benign but potentially life-threatening process related to an abnormal immunologic reaction that results in the proliferation of fibro-inflammatory tissue in the mediastinum. Affected patients are typically young at presentation, but a wide age range has been reported, without a predilection for either sex. Two types of fibrosing mediastinitis have been described: focal and diffuse. The diffuse form may be idiopathic or associated with autoimmunity, usually affects middle-aged and/or elderly patients, and is more common in men. Patients present with signs and symptoms related to obstruction or compression of vital mediastinal structures. CT and MR imaging play a vital role in the diagnosis and management of fibrosing mediastinitis. We present a case of FM in a young male patient with a five-month history of superior vena cava syndrome.

Mot-clés :

Fibrosing Mediastinitis, Granulomatous, Idiopathic, Mri, Ct